Creutzfeldt-Jakob Disease Presenting with Dementia and Mimic a Stroke During One Year: Case Report and Review of Literatures

Authors

  • Habib Farahmand 1. Clinical Research Development Center, Ali Ebn Abitaleb Hospital, Rafsanjan University of Medical Sciences, Rafsanjan, Iran 2. Radiology Department, School of Medicine, Rafsanjan University of Medical Sciences, Rafsanjan, Iran
  • Alireza Vakilian 1. Neurology Department, School of Medicine, Rafsanjan University of Medical Sciences, Rafsanjan, Iran 2. Non-Communicable Diseases Research Center, Rafsanjan University of Medical Sciences, Rafsanjan, Iran
  • Mohaddaseh Fekri 1. Neurology Department, School of Medicine, Rafsanjan University of Medical Sciences, Rafsanjan, Iran 2. Clinical Research Development Center, Ali Ebn Abitaleb Hospital, Rafsanjan University of Medical Sciences, Rafsanjan, Iran

DOI:

https://doi.org/10.31661/gmj.v8i.1357

Keywords:

Creutzfeldt-Jakob Disease, Incidence, Dementia

Abstract

Background: Creutzfeldt-Jakob disease (CJD) is a progressive and fatal prion disease in human and its annual incidence is estimated one per million. Sporadic form of CJD is the most common form of the disease that involved 85% of cases. Case Report: We presented two cases of CJD with the different clinical presentation; a 58-year-old woman who referred with amnesia, depression and a 59-year-old woman with ataxia as her chief complaint. Based on the findings and roled-out the other differential diagnosis, the CJD was confirmed. Both of them died before 12 months after diagnosis. Conclusion: Although CJD is a rare disease with different clinical manifestation, it is considered as one the differential diagnosis of progressive dementia.[GMJ.2019;8:e1357] 

 

References

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Published

2019-01-01

Issue

Section

Case Report/Series